DOI: 10.12890/2017_000714

Silent Adrenal Pheochromocytoma Coexistent with Corticomedullary Hyperplasia: A Case Incidentally Discovered

Authors

  • Luigi Petramala Specialized Center of Secondary Hypertension, Department of Internal Medicine and Medical Specialties, University “Sapienza”, Rome
  • Federica Olmati Specialized Center of Secondary Hypertension, Department of Internal Medicine and Medical Specialties, University “Sapienza”, Rome
  • Antonio Concistrè Specialized Center of Secondary Hypertension, Department of Internal Medicine and Medical Specialties, University “Sapienza”, Rome
  • Vincenza Saraceno Specialized Center of Secondary Hypertension, Department of Internal Medicine and Medical Specialties, University “Sapienza”, Rome
  • Gino Iannucci Specialized Center of Secondary Hypertension, Department of Internal Medicine and Medical Specialties, University “Sapienza”, Rome
  • Antonio Ciardi Department of Surgery “Pietro Valdoni”, University “Sapienza”, Rome
  • Giorgio De Toma Department of Surgery “Pietro Valdoni”, University “Sapienza”, Rome
  • Claudio Letizia Specialized Center of Secondary Hypertension, Department of Internal Medicine and Medical Specialties, University “Sapienza”, Rome

claudio.letizia@uniroma1.it

Keywords

Adrenal Incidentaloma, Subclinical Hypercortisolism, Pheochromocytoma, adrenal hyperplasia

Abstract

Introduction: Pheochromocytoma (PHEO) is a rare catecholamine-producing tumour arising from chromaffin cells in the sympatho-adrenal system, and can present as asymptomatic adrenal incidentaloma (AI).

Patient: We describe the case of a 61-year-old woman with a right adrenal mass incidentally discovered, who was biochemically characterized with subclinical hypercortisolism (SH). The patient was scheduled for adrenalectomy because of increasing seizure of the right adrenal gland with a haemorrhagic and focal pseudocystic appearance macroscopically, incidental histological and immunohistochemical PHEO, and micronodular cortico-adrenal hyperplasia.

Discussion: This report describes a rare case of incidental non-functioning PHEO coexisting with corticomedullary hyperplasia and SH.

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References

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Published

2017-10-06

Issue

Vol. 4 No. 10 (2017)

How to Cite

1.
Petramala L, Olmati F, Concistrè A, Saraceno V, Iannucci G, Ciardi A, et al. Silent Adrenal Pheochromocytoma Coexistent with Corticomedullary Hyperplasia: A Case Incidentally Discovered. EJCRIM [Internet]. 2017 Oct. 6 [cited 2026 Nov. 4];4(10). Available from: https://ejcrim.com/index.php/ejcrim/article/view/714