DOI: 10.12890/2017_000733
Right Ventricle Outflow Obstruction in Biventricular Hypertrophic Cardiomyopathy in Amyloidosis
Authors
dr.hamzasanoussi@gmail.com
Keywords
Biventricular hypertrophic cardiomyopathy, right ventricle outflow tract, amyloidosis, low voltage.Abstract
Light-chain (AL) amyloidosis is the most common type of amyloidosis; cardiac involvement is rare but has a poor prognosis. Biventricular hypertrophic cardiomyopathy is an exceptional finding in amyloidosis and its association with obstructive right ventricular gradient is even rarer. We report the case of a male patient with biventricular hypertrophy suggesting amyloidosis, with an obstructive gradient in the right ventricle.
References
- Desport E, Bridoux F, Sirac C, Delbes S, Bender S, Fernandez B et al. AL amyloidosis. Orphanet J Rare Dis 2012;7:54.
- Falk RH. Diagnosis and management of the cardiac amyloidoses. Circulation 2005;112:2047–2060.
- Philippakis AA, Falk RH. Cardiac amyloidosis mimicking hypertrophic cardiomyopathy with obstruction: treatment with disopyramide. Circulation 2012;125:1821–1824.
- Hirapur I, Kolhari VB, Agrawal N, Rajendran R. Significant biventricular obstruction in non-syndromic hypertrophic cardiomyopathy. BMJ Case Rep 2014;2014:bcr2014206271.
- Halwani O, Delgado DH. Cardiac amyloidosis: an approach to diagnosis and management. Expert Rev Cardiovasc Ther 2010;8:1007–1113.