DOI: 10.12890/2024_005015

Budd-Chiari syndrome as an initial manifestation of incomplete systemic lupus erythematosus

Authors

  • Cecilia Porcu Department of Internal Medicine, Ospedale Regionale di Lugano EOC, Lugano, Switzerland
  • Nathalie Merkel Department of Internal Medicine, Ospedale Regionale di Lugano EOC, Lugano, Switzerland
  • Tanja Fusi- Schmidhauser Department of Internal Medicine, Ospedale Regionale di Lugano EOC, Lugano, Switzerland; Department of Rehabilitation and Geriatrics, University of Geneva, Geneva, Switzerland

ceciliaporcu7@gmail.com

Keywords

Budd-Chiari syndrome, Evan’s syndrome, antiphospholipid syndrome, incomplete lupus, autoimmune disorders

Abstract

This article describes a case of a 26-year-old female with a history of Evan’s syndrome who presented with severe exertional dyspnoea and abdominal discomfort. The patient was diagnosed with chronic Budd-Chiari syndrome, a rare vascular disorder characterized by obstruction of the hepatic vein. We discuss the risk factors, the clinical manifestations, and diagnostic methods for Budd-Chiari syndrome, as well as the possible association with an underlying incomplete systemic lupus erythematosus. The importance of close follow-up and timely diagnosis for preventing disease progression and reducing mortality is emphasized. The article concludes by highlighting the need for further monitoring to identify any symptoms or signs suggesting a progression to complete lupus erythematosus.

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References

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Published

2024-12-02

Issue

Vol. 12 No. 1 (2025)

Categories

How to Cite

1.
Porcu C, Merkel N, Fusi- Schmidhauser T. Budd-Chiari syndrome as an initial manifestation of incomplete systemic lupus erythematosus. EJCRIM [Internet]. 2024 Dec. 2 [cited 2026 Nov. 3];12(1). Available from: https://ejcrim.com/index.php/ejcrim/article/view/5015