DOI: 10.12890/2024_004627

A silent cause of shock: autoimmune polyglandular syndromes

Authors

  • Mark Colantonio Department of Medicine, West Virginia University, Morgantown, USA
  • Michelle Hartzell Department of Medicine, West Virginia University, Morgantown, USA
  • Brooke Shannon Department of Medicine, West Virginia University, Morgantown, USA
  • Apoorva Iyer Department of Medicine, Division of Endocrinology, Morgantown, USA

macolantonio@hsc.wvu.edu

Keywords

Adrenal insufficiency, Addison’s disease, Hashimoto’s disease, autoimmune polyglandular syndromes, autoimmune polyendocrine syndrome type 2

Abstract

Addison’s disease is a rare, autoimmune condition leading to the destruction of the adrenal gland. Autoimmune conditions are known to commonly co-occur. When Addison’s disease presents in the setting of autoimmune thyroid disease and/or type 1 diabetes, this condition is termed autoimmune polyendocrine syndrome type II, a rare endocrinopathy found in roughly 1.4-4.5 per 100,000 individuals. Here, we describe a clinical case presenting with hypotension refractory to fluid resuscitation and electrolyte derangements later diagnosed as autoimmune polyendocrine syndrome type II.

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Published

2024-05-27

Issue

Vol. 11 No. 6 (2024)

Categories

How to Cite

1.
Colantonio M, Hartzell M, Shannon B, Iyer A. A silent cause of shock: autoimmune polyglandular syndromes. EJCRIM [Internet]. 2024 May 27 [cited 2026 Nov. 3];11(6). Available from: https://ejcrim.com/index.php/ejcrim/article/view/4627