DOI: 10.12890/2024_004246
Zinner's syndrome and retroperitoneal fibrosis: an unknown association
Authors
ftornero_r@hotmail.com
Keywords
Zinner’s Syndrome, retroperitoneal fibrosis, rare diseases, renal failure, methotrexateAbstract
We report the case of a 24-year-old male presenting with obstructive renal failure, characterised by imaging evidence of a cystic lesion contingent upon the seminal vesicle and concurrent renal agenesis. Initial management involved urinary diversion, followed by outpatient monitoring and subsequent recurrence. Subsequent diagnostic assessments led to the identification of Zinner's syndrome, accompanied by retroperitoneal fibrosis. We present the clinical course, diagnostic methodology and the efficacious implementation of medical-surgical therapeutic interventions, yielding favourable outcomes.
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