DOI: 10.12890/2016_000424

Intravascular Lymphoma as an Uncommon Cause of Anasarca

Authors

  • Eleni Mylona Fifth Department of Medicine, Evangelismos General Hospital, Athens
  • Styliani Golfinopoulou Fifth Department of Medicine, Evangelismos General Hospital, Athens
  • Pelagia Sfakianaki Fifth Department of Medicine, Evangelismos General Hospital, Athens
  • George Kyriakopoulos Pathology Department, Evangelismos General Hospital, Athens
  • Ioannis Tsonis Ematology Department, Evangelismos General Hospital, Athens
  • Theofanis Apostolou Nephrology Department, Evangelismos General Hospital, Athens
  • Christina Vourlakou Pathology Department, Evangelismos General Hospital, Athens
  • Athanasios Skoutelis Evangelismos General Hospital

emylon@med.uoa.gr

Keywords

Anasarca edema, hemophagocytosis, Intravascular lymphoma.

Abstract

Objectives: To report a case of intravascular lymphoma (IVL) in a Caucasian patient who presented with anasarca as his sole clinical sign.

Material and Methods: A man presented with anasarca-type oedema and fatigue. After excluding heart failure, hepatic cirrhosis, nephrotic syndrome, hypothyroidism, AL-amyloidosis and adverse drug reaction which can all cause oedema, we turned our attention to capillary permeability disorders.

Results: Closer review of the bone marrow aspirate demonstrated haemophagocytic histiocytosis, while core, renal and duodenal biopsies showed a B-cell IVL.

Conclusion: The differential diagnosis of anasarca, a relatively common clinical sign, should include IVL although the diagnosis may still be challenging.

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References

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Published

2016-07-27

Issue

Vol. 3 No. 5 (2016)

How to Cite

1.
Mylona E, Golfinopoulou S, Sfakianaki P, Kyriakopoulos G, Tsonis I, Apostolou T, et al. Intravascular Lymphoma as an Uncommon Cause of Anasarca. EJCRIM [Internet]. 2016 Jul. 27 [cited 2026 Nov. 4];3(5). Available from: https://ejcrim.com/index.php/ejcrim/article/view/424