DOI: 10.12890/2023_004073

Association of Sweet's syndrome and Behçet's disease: is it possible? A case report

Authors

  • El houcine El idrissi Department of Internal Medicine, Military Hospital “Oued DAHAB”, Agadir, Morocco
  • El mehdi El aissat Department of Internal Medicine, Military Hospital “Oued DAHAB”, Agadir, Morocco
  • Naoufal Assoufi Department of Internal Medicine, Military Hospital “Oued DAHAB”, Agadir, Morocco 0000-0003-2938-8523
  • Mohamed Tbouda Anatomo-Pathology Department, Military Hospital “Oued DAHAB”, Agadir, Morocco

dr.el.elhoucine@gmail.com

Keywords

behçet’s disease, sweet’s syndrome, pathogenesis, association

Abstract

Introduction: Behçet's disease is a systemic vasculitis characterized by a large clinical polymorphism with a particular frequency of cutaneous signs. Sweet's syndrome is a neutrophilic dermatosis marked by the sudden appearance of painful skin lesions in the form of erythematous papules, nodules or plaques. This syndrome is associated with high fever, neutrophilia and histologically a diffuse infiltrate of neutrophils in the dermis.
Observation: We report the case of a 43-year-old patient followed for Behçet's disease, who developed cutaneous plaques of neutrophilic dermatosis of both upper limbs. The clinical and biological picture was in favor of Sweet's syndrome.
Conclusion: The coexistence of Sweet's syndrome and Behçet's disease is already reported in the literature. The association is however very rare given the differences in the clinical and pathogenic features between the two conditions.

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References

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Published

2023-09-19

Issue

Vol. 10 No. 10 (2023)

How to Cite

1.
El idrissi E houcine, El aissat E mehdi, Assoufi N, Tbouda M. Association of Sweet’s syndrome and Behçet’s disease: is it possible? A case report. EJCRIM [Internet]. 2023 Sep. 19 [cited 2026 Nov. 3];10(10). Available from: https://ejcrim.com/index.php/ejcrim/article/view/4073