DOI: 10.12890/2023_003954

Wells syndrome with generalized oedema

Authors

  • Magdalini Manti First Internal Medicine Department, “Sismanoglio” General Hospital, Athens, Greece
  • Efthymia Pappa First Internal Medicine Department, “Sismanoglio” General Hospital, Athens, Greece
  • Vasiliki Arkouli First Internal Medicine Department, “Sismanoglio” General Hospital, Athens, Greece
  • Leonidas Marinos Department of Hematopathology “Evangelismos” General Hospital, Athens, Greece
  • Constantinos Christopoulos First Internal Medicine Department, “Sismanoglio” General Hospital, Athens, Greece

mantmagda@gmail.com

Keywords

Wells syndrome, Churg-Strauss syndrome, eosinophilia, cellulitis, vasculitis

Abstract

Wells syndrome or eosinophilic cellulitis is a rare and relapsing skin disease which lacks systemic involvement. A skin biopsy is needed to establish a diagnosis. Several precipitating factors have been proposed but no proven causative link has been found. On the other hand, Churg-Strauss syndrome, also known as eosinophilic granulomatosis with polyangiitis (EGPA), an auto-immune disease, is associated with multiorgan, including cutaneous manifestations. We report a case with overlapping features of Wells and Churg-Strauss syndrome, suggesting that these syndromes could be part of the same nosological entity.

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References

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Published

2023-06-19

Issue

Vol. 10 No. 7 (2023)

Categories

How to Cite

1.
Manti M, Pappa E, Arkouli V, Marinos L, Christopoulos C. Wells syndrome with generalized oedema. EJCRIM [Internet]. 2023 Jun. 19 [cited 2026 Nov. 3];10(7). Available from: https://ejcrim.com/index.php/ejcrim/article/view/3954

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