DOI: 10.12890/2022_003577

Rapidly Progressive Bronchiectasis and Pulmonary Fibrosis in Yellow Nail Syndrome with Possible Association with Selective IgM Deficiency

Authors

  • Mohammad Abu-Abaa Internal Medicine, Capital Health Regional Medical Center, Trenton, NJ, USA
  • Mohamed Hassan Internal Medicine, Capital Health Regional Medical Center, Trenton, NJ, USA
  • Bashar Oudah Eisenhower Health, Rancho Mirage, CA, USA
  • Noor Al-Ameri Internal Medicine, Capital Health Regional Medical Center, Trenton, NJ, USA

Mabu-abaa@capitalhealth.org

Keywords

Yellow nail syndrome, bronchiectasis, pulmonary fibrosis, lymphoedema

Abstract

A 67-year-old man with a history of IgM deficiency and pulmonary fibrosis and bronchiectasis was admitted for management of worsening symptoms. Investigations revealed exudative pleural effusion with rapidly progressive bronchiectasis. Although a potential trigger of bronchiectasis and pulmonary fibrosis was not identified despite extensive work-up by several physicians in the past, a bedside observation of yellow dystrophic nails on all extremities revealed the diagnosis. This case report helps to remind clinicians of a rare medical disorder of still uncertain aetiology and no available cure. This case is consistent with a few previous case reports that suggest a potential association with selective immunoglobulin deficiency.

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References

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Published

2022-09-27

How to Cite

1.
Abu-Abaa M, Hassan M, Oudah B, Al-Ameri N. Rapidly Progressive Bronchiectasis and Pulmonary Fibrosis in Yellow Nail Syndrome with Possible Association with Selective IgM Deficiency. EJCRIM [Internet]. 2022 Sep. 27 [cited 2026 Nov. 3];9(9). Available from: https://ejcrim.com/index.php/ejcrim/article/view/3577

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