DOI: 10.12890/2022_003160

Esophageal Bullous Pemphigoid

Authors

  • Catarina Castelo Branco Department of Internal Medicine, Centro Hospitalar Universitário do Porto, Porto, Portugal
  • Tomás Fonseca Department of Internal Medicine, Centro Hospitalar Universitário do Porto, Porto, Portugal
  • Ricardo Marcos-Pinto Department of Gastroenterology, Centro Hospitalar Universitário do Porto, Porto, Portugal

catarinamcbranco@gmail.com

Keywords

Bullous pemphigoid, esophagus, dementia

Abstract

Bullous pemphigoid is a rare autoimmune dermatologic disease that usually occurs in the elderly. Mucous membrane lesions occur in about 10–35% of patients and are almost always limited to the oral mucous membrane. Esophageal involvement is very rare (4% of cases) and usually presents with chest pain, dysphagia, and odynophagia, though patients are frequently asymptomatic. We report the case of newly diagnosed bullous pemphigoid in a 76-year-old man with a past medical history of dementia. He presented with cutaneous manifestations but also severe gastrointestinal bleeding due to extensive esophageal involvement. Although bullous pemphigoid is mainly a skin disease, mucous membrane lesions should not be overlooked as they are associated with an even poorer outcome. A high index of suspicion for esophageal involvement is needed as its presentation can be fatal, as with our patient.

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References

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Published

2022-02-01

Issue

Vol. 9 No. 2 (2022)

How to Cite

1.
Castelo Branco C, Fonseca T, Marcos-Pinto R. Esophageal Bullous Pemphigoid. EJCRIM [Internet]. 2022 Feb. 1 [cited 2026 Nov. 3];9(2). Available from: https://ejcrim.com/index.php/ejcrim/article/view/3160

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