DOI: 10.12890/2021_003073

Haemophagocytic Lymphohistiocytosis as a Complication of Israeli Spotted Fever

Authors

  • Maria Margarida Andrade Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Ana Gorgulho Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Rita Tinoco Magalhães Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Rita Valadas Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Luís Miguel Pereira Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Sara Freire Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal
  • Diogo Cruz Internal Medicine Department, Hospital de Cascais Dr. José de Almeida, Alcabideche, Portugal; Faculty of Medicine, University of Lisbon, Lisbon, Portugal

mariamargaridaandrade@gmail.com

Keywords

Rickettsiosis, spotted fever, haemophagocytic, purpura fulminans, polyneuropathy

Abstract

Rickettsia spp. human infection is endemic in Portugal in the form of Mediterranean spotted fever caused by R. conorii subsp. conorii and Israeli spotted fever (ISF) caused by R. conorii subsp. israelensis. We describe a rare case of haemophagocytic lymphohistiocytosis (HLH) due to ISF, with atypical manifestations. We highlight the need for clinical suspicion for this diagnosis and the importance of timely intervention and support.

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References

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Published

2022-01-17

Issue

Vol. 9 No. 1 (2022)

How to Cite

1.
Andrade MM, Gorgulho A, Tinoco Magalhães R, Valadas R, Pereira LM, Freire S, et al. Haemophagocytic Lymphohistiocytosis as a Complication of Israeli Spotted Fever. EJCRIM [Internet]. 2022 Jan. 17 [cited 2026 Nov. 3];9(1). Available from: https://ejcrim.com/index.php/ejcrim/article/view/3073

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