DOI: 10.12890/2021_002736
Hypoplastic Coronary Artery Disease Presenting with Ventricular Fibrillation Cardiac Arrest
Authors
abraguo001@gmail.com
Keywords
Hypoplastic coronary artery disease, cardiac arrestAbstract
Hypoplastic coronary artery disease is a rare congenital anomaly that may present with ischaemic heart disease, heart failure or sudden cardiac death (SCD). We describe a case of cardiac arrest in a healthy young man. Work-up revealed a hypoplastic left anterior descending artery. The patient underwent cardioverter-defibrillator implantation for secondary prevention.
References
- De Giorgio F, Abbate A, Stigliano E, Capelli A, Arena V. Hypoplastic coronary artery disease causing sudden death. Report of two cases and review of the literature. Cardiovasc Pathol 2010;19:107–111.
- Fraisse A, Quilici J, Canavy I, Savin B, Aubert F, Bory M. Myocardial infarction in children with hypoplastic coronary arteries. Circulation 2000;101:1219–1222.
- Sim DS, Jeong MH, Choi S, Yoon NS, Yoon HJ, Moon JY, et al. Myocardial infarction in a young man due to a hypoplastic coronary artery. Korean Circ J 2009;39:163–167.
- McFarland C, Swamy RS, Shah A. Hypoplastic coronary artery disease: a rare cause of sudden cardiac death and its treatment with an implantable defibrillator. J Cardiol Cases 2011;14:148–151.
- Shi X, Liu J, Wu J, Hua Y, Zhou K, Li Y. Hypoplastic coronary arteries in a child with a mutation in Notch1: a case report. Medicine (Baltimore) 2020;99(33):e21355.
- Riede FN, Bulla S, Grundmann S, Werner M, Riede U, Otto C. Isolated hypoplastic circumflex coronary artery: a rare cause of haemorrhagic myocardial infarction in a young athlete. Diagn Pathol 2013;8:91.
- Foley TR, Krantz MJ. Resuscitated sudden cardiac death due to diminutive coronary artery syndrome. HeartRhythm Case Rep 2016;30:141–144.
- Harris SL, Lubitz SA. Clinical and genetic evaluation after sudden cardiac arrest. J Cardiovasc Electrophysiol 2020;31:570–578.
- Kafrouni G, Khan AH, Wolfsen JL. Single right coronary artery: clinical and angiographic findings with surgical management. Ann Thorac Surg 1981;32:80–84.
Published
2021-08-02
Issue
How to Cite
1.
Guo A, Bakhshi H, O'Hara J, Genovese L, Fein A, Maghsoudi A, et al. Hypoplastic Coronary Artery Disease Presenting with Ventricular Fibrillation Cardiac Arrest. EJCRIM [Internet]. 2021 Aug. 2 [cited 2026 Nov. 4];8(8). Available from: https://ejcrim.com/index.php/ejcrim/article/view/2736