DOI: 10.12890/2021_002312
Congenital Inferior Vena Cava Agenesis with Ulceration and Deep Vein Thrombosis
Authors
melanie.menning@unmc.edu
Keywords
Inferior vena cava atresia, IVCA, ulcers, deep vein thrombus, DVTAbstract
Objectives: This is one of the few case reports of congenital inferior vena cava atresia (IVCA) with extensive bilateral lower extremity ulcers.
Background: IVCA is a congenital anomaly characterized by poor venous return in the lower extremities with increased risk of deep vein thrombi (DVTs) and, rarely, non-healing ulcers.
Results: A 45-year-old woman with history significant for DVTs presented with extensive bilateral lower extremity ulcers, and a CT scan revealed congenital IVCA. Oedema management, DVT prevention, routine wound care and skin grafts resolved the ulcers.
Conclusion: Congenital venous abnormalities should be included in the differential diagnosis of multiple unprovoked DVTs and non-healing ulcers.
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