DOI: 10.12890/10.12890/2015_000206

Hypokalemic Paralysis as First Manifestation of Sjögren Syndrome

Authors

  • Jorge Arsénio Ruivo Medicine 1 Department, Hospital Santa Maria, Lisbon, Portugal https://sites.google.com/site/jorgearuivo/
  • Ana Tornada Medicine 1 Department, Hospital Santa Maria, Lisbon, Portugal
  • Pawel Sierzputowski Medicine 1 Department, Hospital Santa Maria, Lisbon, Portugal
  • Paula Alcântara Medicine 1 Department, Hospital Santa Maria, Lisbon, Portugal

jorgearsenioruivo@gmail.com

Abstract

Objectives: To highlight systemic involvement features in Sjögren Syndrome (SS).

Materials and methods: A case of a 32-year-old woman presenting with flaccid tetraparesis, in the setting of severe hypokalaemia, is described.

Results: Additional evaluation confirmed primary SS with type 1 renal tubular acidosis (RTA1) and gammaglobulin-mediated vasculitis. A significant clinical improvement was achieved following adequate treatment.

Conclusion: Extra-glandular involvement in SS is usually due to autoimmune lymphocytic infiltration and severe complications can be avoided if there is a prompt diagnosis.

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References

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Published

2015-04-25

Issue

Vol. 2 No. 2 (2015)

How to Cite

1.
Ruivo JA, Tornada A, Sierzputowski P, Alcântara P. Hypokalemic Paralysis as First Manifestation of Sjögren Syndrome. EJCRIM [Internet]. 2015 Apr. 25 [cited 2026 Nov. 3];2(2). Available from: https://ejcrim.com/index.php/ejcrim/article/view/206