DOI: 10.12890/2015_000199

Extensive Calcinosis in an Adult Nigerian Woman with Dermatomyositis

Authors

  • Olufemi Adelowo Rheumatology Unit, Department of Internal Medicine, Lagos State University Teaching Hospital, Ikeja, Lagos, Nigeria
  • Obiageli John-maduagwu Rheumatology Unit, Department of Internal Medicine, Federal Medical Centre, Owerri, Imo, Nigeria
  • Hamidu Ahmed Rheumatology Unit, Department of Internal Medicine, Aminu Kano Teaching Hospital, Kano, Nigeria
  • Louis Olisaka Rheumatology Unit, Department of Internal Medicine, Federal Medical Centre, Abakaliki, Ebonyi, Nigeria

femiadelowo2003@yahoo.com

Abstract

Objectives: Extensive calcinosis in a patient with dermatomyositis is a rare clinical presentation in adults. The aim of this report is to present the clinical and radiographic features of a 25-year-old woman with dermatomyositis and extensive calcinosis.

Case Presentation: A 25-year-old woman with extensive calcinosis on background dermatomyositis is described.

Results: The clinical and radiographic features of the patient were consistent with dermatomyositis complicated by extensive calcinosis in an adult.

Conclusion: Dermatomyositis with extensive calcinosis is a rare clinical presentation in adults.

View the entire article

Downloads

References

  1. Bohan A, Peter JB. Polymyositis and dermatomyositis. N Eng J Med 1975;292:344–347.
  2. Adelowo O, Nwankwo M, Olaosebikan H. Juvenile dermatomyositis in a Nigerian girl. BMJ Case Reports 2014; doi: 10.1136/bcr-2013-202132.
  3. Faller G, Mistry BJ, Tikly M. Juvenile dermatomyositis in South African children is characterised by frequent dystrophic calcifications: a cross sectional study. Paediatr Rheumatol 2014;12:2.
  4. Adelowo OO, Edomwonyi U, Olaosebikan H. Inflammatory myopathies in Nigerians: case series and literature review. Afr J Med Medical Sci 2013;42:143–149.
  5. Bahar D, Phillips TJ. Adult-onset dermatomyositis complicated by calcinosis cutis. Wounds 2004;16:364–370.
  6. Majithia V, Harisdangkul V. Mycophenolate mofetil (Cellcept): an alternative therapy for autoimmune inflammatory myopathy. Rheumatology 2005;44:386–389.
  7. Smoyer-Tomic KE, Amato AA, Fernandes AW. Incidence and prevalence of idiopathic inflammatory myopathies among commercially insured, Medicare supplemental insured, and Medicaid enrolled populations: an administrative claims analysis. BMC Musculoskelet Disord 2012;13:1–13.
  8. Shah R, Ellis S. Subcutaneous fat calcinosis in adult onset dermatomyositis. BMJ Case Reports 2011; doi:10.1136/bcr.05.2011.4268.
  9. Presley BC, Bush JS, Watson SC. Dermatomyositis with extensive calcification in an adult. West J Emerg Med 2012;13:136–138.
  10. Terroso G, Bernardes M, Aleixo A, Madureira P, Vieira R, Bernardo A, et al. Therapy of calcinosis universalis complicating adult dermatomyositis. Acta Reumatol Port 2013;8:44–48.
  11. Souza FH, Barros TB, Levy-Neto M, Shinjo SK. Adult dermatomyositis: experience of a Brazilian tertiary care centre. Rev Bras Reumatol 2012;52: 892–902.
  12. Callen JP. Dermatomyositis. Lancet 2000;355:53–57.
  13. Fisler RE, Liang MG, Fuhlbrigge RC, Yalcindag A, Sundel RP. Aggressive management of juvenile dermatomyositis results in improved outcome and decreased incidence of calcinosis. J Am Acad Dermatol 2002;47:505–511.
  14. Pachman LM, Boskey AL. Clinical manifestation and pathogenesis of hydroxyapatite crystal deposition in juvenile dermatomyositis. Curr Rheumatol Rep 2006;8:236–243.
  15. Santili C, Akkari M, Waisberg G, Kessler C, Alcantara T. Calcinosis universalis: a rare diagnosis. J Pediatr Orthop B 2005;14:294–298.
  16. Chander S, Gordon P. Soft tissue and subcutaneous calcification in connective tissue diseases. Curr Opin Rheumatol 2012;24:158–164. doi: 10.1097/BOR.0b013e32834ff5cd.
  17. Abdallah-Lotf M, Grasland A, Vinceneux P, Sigal-Grinberg M. Regression of calcinosis cutis with diltiazem in adult dermatomyositis. Eur J Dermatol 2005;15:102–104.
  18. Fleury J, Guillet G, Anyfantakis V, Huguier V. Unusual calcinosis of muscular legs in a 37 year old patient with a history of juvenile dermatomyositis. Eur J Dermatol 2010;20:647–648.
  19. Slimani S, Abdessemed A, Haddouche A, Ladjouze-Rezig A. Complete resolution of universal calcinosis in a patient with juvenile dermatomyositis using pamidronate. Joint Bone Spine 2010;77:70–72.
  20. Marco Puche A, Calvo Penades I, Lopez Montesinos B. Effectiveness of the treatment with intravenous pamidronate in calcinosis in juvenile dermatomyositis. Clin Exp Rheumatol 2010;28:135–140.

Published

2015-04-22

How to Cite

1.
Adelowo O, John-maduagwu O, Ahmed H, Olisaka L. Extensive Calcinosis in an Adult Nigerian Woman with Dermatomyositis. EJCRIM [Internet]. 2015 Apr. 22 [cited 2026 Nov. 3];2(2). Available from: https://ejcrim.com/index.php/ejcrim/article/view/199