DOI: 10.12890/2020_001939

Cutaneous Angiosarcoma in an Unusual Location and Without Predisposing Factors

Authors

  • Ana Oliveira Monteiro Department of Internal Medicine, Centro Hospitalar Universitário de São João, Porto, Portugal
  • Inês Branco Ferreira Department of Internal Medicine, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • Artur César Department of Dermatology and Venereology, Centro Hospitalar de Vila Nova de Gaia/Espinho, Porto, Portugal
  • Alberto Mota Department of Dermatology and Venereology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S.João, Porto, Portugal
  • Jorge Pinheiro Department of Pathology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • José Manuel Lopes Department of Pathology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • M Teresa Cardoso Department of Internal Medicine, Centro Hospitalar Universitário de S. João, Porto, Portugal

ana.galraoom@gmail.com

Keywords

Cutaneous angiosarcoma, lower limbs, predisposing factors, immunohistochemistry

Abstract

Cutaneous angiosarcoma is a rare, highly malignant tumour of vascular endothelial origin. It usually arises in the skin and superficial soft tissue, mostly on the head and neck. It presents as a variety of lesions, and so is considered a great mimicker, leading to a delay in diagnosis and evidencing the importance of biopsy with immunohistochemistry confirmation. There are few reports of extremity involvement in patients with pre-existing chronic lymphoedema, or exposure to radiation therapy. We report the case of an 82-year-old woman with lower limb extensive cutaneous involvement, distant metastatic disease, and poor therapy response. Its rare location without predisposing factors highlights the need to raise awareness about this disease

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References

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Published

2020-09-25

Issue

Vol. 7 No. 12 (2020)

How to Cite

1.
Monteiro AO, Branco Ferreira I, César A, Mota A, Pinheiro J, Manuel Lopes J, et al. Cutaneous Angiosarcoma in an Unusual Location and Without Predisposing Factors. EJCRIM [Internet]. 2020 Sep. 25 [cited 2026 Nov. 3];7(12). Available from: https://ejcrim.com/index.php/ejcrim/article/view/1939