Right Ventricle Outflow Obstruction in Biventricular Hypertrophic Cardiomyopathy in Amyloidosis
  • Hamza Sanoussi
    Cardiology department 'B', IBN Sina Hospital, Rabat
  • Najla Kourireche
    Cardiology department 'B', IBN Sina Hospital, Rabat
  • Latifa Oukerraj
    Cardiology department 'B', IBN Sina Hospital, Rabat
  • Mohammed Cherti
    Cardiology department 'B', IBN Sina Hospital, Rabat

Keywords

Biventricular hypertrophic cardiomyopathy, right ventricle outflow tract, amyloidosis, low voltage.

Abstract

Light-chain (AL) amyloidosis is the most common type of amyloidosis; cardiac involvement is rare but has a poor prognosis. Biventricular hypertrophic cardiomyopathy is an exceptional finding in amyloidosis and its association with obstructive right ventricular gradient is even rarer. We report the case of a male patient with biventricular hypertrophy suggesting amyloidosis, with an obstructive gradient in the right ventricle.

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References

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    Published: 2017-10-02
    Issue: Vol. 4 No. 9 (view)


    How to cite:
    1.
    Sanoussi H, Kourireche N, Oukerraj L, Cherti M. Right Ventricle Outflow Obstruction in Biventricular Hypertrophic Cardiomyopathy in Amyloidosis. EJCRIM 2017;4 doi:10.12890/2017_000733.