Myxoma involving the pulmonary valve – A case report of an atypical cardiac tumor, treated using an unusual approach
  • Geeta Bhagia
    Rochester General Hospital, Rochester, USA
  • Nasir Hussain
    UHS Wilson Medical Center, Johnson City, USA
  • Fnu Arty
    Monmouth Medical Center, Long Branch, USA
  • Mithun Chakravarthy
    Allegheny General Hospital, Pittsburgh, USA
  • Moneal Shah
    Allegheny General Hospital, Pittsburgh, USA

Keywords

Atypical myxoma, pulmonary valve, percutaneous removal, malignant and benign cardiac tumors

Abstract

Background: Atypical myxoma has been reported in various locations in the heart, however, myxoma involving the pulmonary valve is rare. Here we present a case of pulmonic valve myxoma which was resected via a percutaneous approach.
Case Report: A 66-year-old female with known metastatic adenocarcinoma of the lung, and chronic obstructive pulmonary disease presented with acute onset shortness of breath for two days. The patient experienced respiratory arrest en-route to the hospital and required intubation. Computed tomography angiography (CTA) of the chest revealed a new 1.4 x 1.6 cm intracardiac mass along the pulmonary valve. Further evaluation with cardiac magnetic resonance imaging revealed it to be a large vascular tumor on the ventricular side of the pulmonary valve, attached with a narrow stalk. Due to high surgical risk, the patient underwent transesophageal echocardiographic guided percutaneous removal of the mass. Pathology confirmed the mass to be a myxoma.
Conclusion: Atypical myxoma should be considered in the differential diagnosis of valvular masses. Percutaneous resection of valvular masses may be feasible in high-risk surgical patients.

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    Published: 2024-05-22
    Issue: 2024: Vol 11 No 6 (view)

    How to cite:
    1.
    Bhagia G, Hussain N, Arty F, Chakravarthy M, Shah M. Myxoma involving the pulmonary valve – A case report of an atypical cardiac tumor, treated using an unusual approach. EJCRIM 2024;11 doi:10.12890/2024_004519.