Huge Tracheal Diverticulum in a Patient with Mounier-Kuhn Syndrome

  • Michele Mondoni Respiratory Unit, San Paolo Hospital, Dept. of Health Sciences, Università degli Studi di Milano, Milan, Italy
  • Paolo Carlucci Respiratory Unit, San Paolo Hospital, Dept. of Health Sciences, Università degli Studi di Milano, Milan, Italy
  • Elena Maria Parazzini Respiratory Unit, San Paolo Hospital, Dept. of Health Sciences, Università degli Studi di Milano, Milan, Italy
  • Paolo Busatto U.O. Pneumologia, Ospedale San Lucca, USL Nordovest Toscana, Lucca, Italy
  • Stefano Centanni Respiratory Unit, San Paolo Hospital, Dept. of Health Sciences, Università degli Studi di Milano, Milan, Italy

Keywords

tracheal diverticulum, tracheocele, Mounier-Kuhn syndrome, bronchoscopy

Abstract

Tracheal diverticulum is a rare benign entity. Tracheobronchomegaly (TBM), also known as Mounier-Kuhn syndrome, is a rare disorder characterized by marked dilation of the trachea and main bronchi, associated with thinning or atrophy of the elastic tissue. Because of the weakened trachea and increased intraluminal pressure related to chronic cough, some patients may develop mucosal herniation leading to tracheal diverticulosis. We report the case of a patient with TBM with a huge tracheal diverticulum, diagnosed by bronchoscopy and computed tomography with three-dimensional reconstruction. To our knowledge this is the largest tracheal diameter described in a patient affected by this syndrome.

VIEW THE ENTIRE ARTICLE

References

  • Schwartz M, Rossoff L. Tracheobronchomegaly. Chest 1994;106:1589–1590.
  • Payandeh J, McGillivray B, McCauley G, Wilcox P, Swiston JR, Lehman A. A clinical classification scheme for tracheobronchomegaly (Mounier-Kuhn syndrome). Lung2015;193:815–822.
  • Soto-Hurtado EJ, Peñuela-Ruiz L, Rivera-Sanchez I, Torres-Jimenez J. Tracheal diverticulum: a review of the literature. Lung 2006;184:303–307.
  • Rojas J, Bostanci K, Katsenos S, Becker HD. Tracheal diverticulum. J Bronchol Intervent Pulmonol 2011;18:91–93.
  • Polverosi R, Carloni A, Poletti V. Tracheal and main bronchial diverticula: the role of CT. Radiol Med 2008;113:181–189.
  • Published: 2016-07-27

    Issue: Vol. 3 No. 5 (view)

    Section: Articles

    How to cite:
    1.
    Mondoni M, Carlucci P, Parazzini EM, Busatto P, Centanni S. Huge Tracheal Diverticulum in a Patient with Mounier-Kuhn Syndrome. EJCRIM 2016;3 doi:10.12890/2016_000419.