Angina pectoris as a manifestation of ALCAPA syndrome in a 20-year-old female: a case report and review of literature

  • Leila Bigdelu Cardiovascular Medicine Division, Vascular Surgery Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
  • Ossama Maadarani Consultant internal medicine and cardiology
  • Ali Azari Cardiovascular Medicine Division, Vascular Surgery Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
  • Ali Heidari-Bakavoli Department of Imaging, Razavi Hospital, Mashhad, Iran
  • Zouheir Bitar Critical Care Unit, Internal Medical Department, Ahmadi Hospital (KOC), Kuwait
DOI: https://doi.org/10.12890/2023_003962

Keywords

ALCAPA, echocardiography, angina pectoris

Abstract

Anomalous left coronary artery from the pulmonary artery (ALCAPA) is considered a rare congenital heart disease where the take-off of the left coronary artery abnormally originates from the pulmonary artery instead of left aortic sinus. It is associated with a high mortality rate in the first year of life and sudden death in adults if left untreated. We report an adult form of ALCAPA syndrome in a 20-year-old female who presented with anginal pain for the previous few months. Unfortunately, the patient was hesitant to have surgery at the time.

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    • Published: 2023-06-26

    Issue: 2023: Vol 10 No 7 (view)

    Section: Articles

    How to cite:
    1.
    Bigdelu L, Maadarani O, Azari A, Heidari-Bakavoli A, Bitar Z. Angina pectoris as a manifestation of ALCAPA syndrome in a 20-year-old female: a case report and review of literature. EJCRIM 2023;10 doi:10.12890/2023_003962.

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