New-onset cardiac amyloidosis while in remission from systemic AL amyloidosis
  • Abiodun Idowu
    Department of Internal Medicine, Einstein Medical Center, Philadelphia, Pennsylvania, USA https://orcid.org/0000-0003-4702-9233
  • Lillian Tung
    Department of Internal Medicine, Rush University Medical Center, Chicago, Illinois, USA
  • Catherine Chu
    Rush University Medical College, Chicago, Illinois, USA
  • Jamario Skeete
    Division of Cardiology, Rush University Medical Center, Chicago, Illinois, USA
  • Agne Paner
    Division of Hematology/Oncology/Cell Therapy, Rush University Medical Center, Chicago, Illinois, USA
  • Tochukwu Okwuosa
    Division of Cardiology, Section of Cardio-Oncology, Rush University Medical Center, Chicago, Illinois, USA

Keywords

Light chain, plasma cell, cardiac amyloidosis

Abstract

In light chain amyloidosis, a reduction in dFLC to below 40 mg/l is a prerequisite for organ recovery as nearly half of the patients who achieve very good partial haematological responses have improvement in the function of the involved organ. We describe a patient who developed new-onset cardiac amyloidosis despite a post-treatment reduction in dFLC to <10 mg/l.

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References

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    Published: 2023-02-28
    Issue: 2023: Vol 10 No 2 (view)

    How to cite:
    1.
    Idowu A, Tung L, Chu C, Skeete J, Paner A, Okwuosa T. New-onset cardiac amyloidosis while in remission from systemic AL amyloidosis . EJCRIM 2023;10 doi:10.12890/2023_003768.

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