Pulmonary Arterial Hypertension Associated With Primary Sjögren’s Syndrome: An Unusual Association
  • Pedro Ribeirinho-Soares
    Internal Medicine Department, University Hospital Center of São João, Porto, Portugal; Faculty of Medicine, University of Porto, Porto, Portugal https://orcid.org/0000-0002-5534-8077
  • Estela Sousa
    Internal Medicine Department, University Hospital Center of São João, Porto, Portugal
  • Inês Silva
    Internal Medicine Department, University Hospital Center of São João, Porto, Portugal
  • Jorge Almeida
    Internal Medicine Department, University Hospital Center of São João, Porto, Portugal; Faculty of Medicine, University of Porto, Porto, Portugal

Keywords

Primary Sjögren’s syndrome, pulmonary artery hypertension

Abstract

Pulmonary arterial hypertension (PAH) is an increasingly recognised clinical entity that is associated with connective tissue disease (CTD) in up to one quarter of all diagnoses. Sjögren’s syndrome (SS) is a chronic autoimmune disease characterised by ocular and oral dryness resulting from lacrimal and salivary gland dysfunction. Additionally, SS may involve virtually any organ system and, as a result, the disease is characterised by pleomorphic clinical manifestations. However, SS-PAH reports are scarce, and the area remains insufficiently studied. We present a case of a 75-year-old female with a new diagnosis of PAH and SS.

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    Published: 2022-11-10
    Issue: 2022: Vol 9 No 11 (view)

    How to cite:
    1.
    Ribeirinho-Soares P, Sousa E, Silva I, Almeida J. Pulmonary Arterial Hypertension Associated With Primary Sjögren’s Syndrome: An Unusual Association. EJCRIM 2022;9 doi:10.12890/2022_003606.

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