Reversible Cerebral Vasospasm in Acute Intermittent Porphyria: A Case Report and Review of the Literature
  • Attout Hassene
    Internal Medicine Unit, General Hospital Les Cevennes, Alés, France
  • Stephane Guez
    Internal Medicine Unit, Pellegrin Teaching Hospital, Bordeaux, France


Porphyria, cerebral infarction, vasospasm


The porphyrias are rare inherited diseases of heme biosynthesis which can involve the nervous system. The most common neurological manifestations of acute intermittent porphyria are autonomic visceral neuropathy, peripheral motor neuropathy, and central nervous system dysfunction. In rare cases, patients with acute intermittent porphyria have presented with cerebral infarction, suggested to be due to vasospasm in cerebral arteries. We report a case of reversible vasospasm in porphyric encephalopathy demonstrated by both magnetic resonance and conventional angiography. Unexplained abdominal pain occurred before the onset of neurological symptoms.



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    Published: 2022-09-12
    Issue: 2022: Vol 9 No 9 (view)

    How to cite:
    Hassene A, Guez S. Reversible Cerebral Vasospasm in Acute Intermittent Porphyria: A Case Report and Review of the Literature. EJCRIM 2022;9 doi:10.12890/2022_003543.