Unicentric Castleman Disease and Pheochromocytoma

  • Rosana Maia Department of Medicine, Unidade Local de Saúde do Alto Minho, Viana do Castelo, Portugal
  • Joana Couto Department of Medicine, Unidade Local de Saúde do Alto Minho, Viana do Castelo, Portugal
  • José Diogo Martins Department of Medicine, Unidade Local de Saúde do Alto Minho, Viana do Castelo, Portugal
  • Edgar Torre Department of Medicine, Unidade Local de Saúde do Alto Minho, Viana do Castelo, Portugal
  • Diana Guerra Department of Medicine, Unidade Local de Saúde do Alto Minho, Viana do Castelo, Portugal

Keywords

IL-6, adenomegaly, adrenal mass, pheochromocytoma, Castleman disease

Abstract

Castleman disease is an uncommon and heterogenous lymphoproliferative disorder which is classified as unicentric or multicentric depending on the number of lymph nodes involved. Each type has a different clinical presentation, aetiology, treatment and prognosis. We report the case of a young woman who presented with cervical lymphadenopathy and a retroperitoneal mass, and was diagnosed with unicentric Castleman disease and pheochromocytoma. We describe the diagnostic steps, the complications that developed, and the importance of the differential diagnosis in the evaluation of these patients.

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References

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  • Published: 2022-01-14

    Issue: 2022: LATEST ONLINE (view)

    Section: Articles

    How to cite:
    1.
    Maia R, Couto J, Martins JD, Torre E, Guerra D. Unicentric Castleman Disease and Pheochromocytoma. EJCRIM 2022;2 doi:10.12890/2022_003068.

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