Immune Thrombocytopenia: A Rare Presentation of Pulmonary Sarcoidosis
  • Mariana da Silva Leal
    Internal Medicine Department, Centro Hospitalar do Baixo Vouga, Aveiro, Portugal
  • Carolina Amado
    Internal Medicine Department, Centro Hospitalar do Baixo Vouga, Aveiro, Portugal
  • Bárbara Paracana
    Internal Medicine Department, Centro Hospitalar do Baixo Vouga, Aveiro, Portugal
  • Flávio Pereira
    Internal Medicine Department, Centro Hospitalar do Baixo Vouga, Aveiro, Portugal
  • Mariana Sousa
    Internal Medicine Department, Centro Hospitalar do Baixo Vouga, Aveiro, Portugal
  • Aurora Mendes
    Pneumology Department, Centro Hospitalar do Baixo Vouga, Aveiro, Portugal

Keywords

Immune thrombocytopenia, immunosuppressive therapy, sarcoidosis

Abstract

Thrombocytopenia may be the initial presentation of sarcoidosis, which is a systemic granulomatous disorder. Various pathophysiological mechanisms have been identified. Immune thrombocytopenia often has a severe presentation but may respond favourably to immunosuppressive therapy. There are no guidelines for the treatment of thrombocytopenia in sarcoidosis. However, in emergency situations with major bleeding, it seems reasonable to apply the current guidelines recommended for immune thrombocytopenia.
The authors report a case of sarcoidosis presenting with severe thrombocytopenia, petechial rash, and nasal and gingival bleeding.

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    Published: 2021-12-20
    Issue: 2021: Vol 8 No 12 (view)

    How to cite:
    1.
    da Silva Leal M, Amado C, Paracana B, Pereira F, Sousa M, Mendes A. Immune Thrombocytopenia: A Rare Presentation of Pulmonary Sarcoidosis. EJCRIM 2021;8 doi:10.12890/2021_003060.