Foix-Alajouanine Syndrome Mimicking Longitudinally Extensive Transverse Myelitis

  • Anirudha S Rathnam Department of Neurology, Henry Ford Health System, Detroit, Michigan, USA
  • Anza B Memon Department of Neurology, Henry Ford Health System, Detroit, Michigan, USA; Wayne State University, School of Medicine, Detroit, Michigan, USA

Keywords

Longitudinally extensive transverse myeliti, LETM, spinodural arteriovenous fistula, SDAF, artery of Adamkiewicz

Abstract

Foix-Alajouanine syndrome is an arteriovenous malformation causing subacute congestive myelopathy that can lead to progressive paraplegia. It typically affects the lower thoracic and lumbosacral levels. Arteriovenous fistula (AVF) leads to increased venous pressure, decreasing the arteriovenous pressure gradient and leading to a decrease in spinal cord perfusion, oedema and necrosis. Early recognition and surgical intervention can result in a good prognosis.

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References

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Published: 2020-11-10

Issue: Vol 8 No 1 (view)

Section: Articles

How to cite:
1.
Rathnam AS, Memon AB. Foix-Alajouanine Syndrome Mimicking Longitudinally Extensive Transverse Myelitis. EJCRIM 2020;8 doi:10.12890/2020_002063.