Hypokalemic Paralysis as First Manifestation of Sjögren Syndrome
  • Jorge Arsénio Ruivo
    Medicine 1 Department, Hospital Santa Maria, Lisbon, Portugal
  • Ana Tornada
    Medicine 1 Department, Hospital Santa Maria, Lisbon, Portugal
  • Pawel Sierzputowski
    Medicine 1 Department, Hospital Santa Maria, Lisbon, Portugal
  • Paula Alcântara
    Medicine 1 Department, Hospital Santa Maria, Lisbon, Portugal

Abstract

Objectives: To highlight systemic involvement features in Sjögren Syndrome (SS).

Materials and methods: A case of a 32-year-old woman presenting with flaccid tetraparesis, in the setting of severe hypokalaemia, is described.

Results: Additional evaluation confirmed primary SS with type 1 renal tubular acidosis (RTA1) and gammaglobulin-mediated vasculitis. A significant clinical improvement was achieved following adequate treatment.

Conclusion: Extra-glandular involvement in SS is usually due to autoimmune lymphocytic infiltration and severe complications can be avoided if there is a prompt diagnosis.

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    Published: 2015-04-25
    Issue: Vol. 2 No. 2 (2015) (view)


    How to cite:
    1.
    Ruivo JA, Tornada A, Sierzputowski P, Alcântara P. Hypokalemic Paralysis as First Manifestation of Sjögren Syndrome. EJCRIM 2015;2 doi:10.12890/10.12890/2015_000206.