Hypokalemic Paralysis as First Manifestation of Sjögren Syndrome
Objectives: To highlight systemic involvement features in Sjögren Syndrome (SS).
Materials and methods: A case of a 32-year-old woman presenting with flaccid tetraparesis, in the setting of severe hypokalaemia, is described.
Results: Additional evaluation confirmed primary SS with type 1 renal tubular acidosis (RTA1) and gammaglobulin-mediated vasculitis. A significant clinical improvement was achieved following adequate treatment.
Conclusion: Extra-glandular involvement in SS is usually due to autoimmune lymphocytic infiltration and severe complications can be avoided if there is a prompt diagnosis.
Issue: Vol. 2 No. 2 (2015) (view)