Cutaneous Angiosarcoma in an Unusual Location and Without Predisposing Factors
  • Ana Oliveira Monteiro
    Department of Internal Medicine, Centro Hospitalar Universitário de São João, Porto, Portugal
  • Inês Branco Ferreira
    Department of Internal Medicine, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • Artur César
    Department of Dermatology and Venereology, Centro Hospitalar de Vila Nova de Gaia/Espinho, Porto, Portugal
  • Alberto Mota
    Department of Dermatology and Venereology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S.João, Porto, Portugal
  • Jorge Pinheiro
    Department of Pathology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • José Manuel Lopes
    Department of Pathology and Faculty of Medicine of the University of Porto, Centro Hospitalar Universitário de S. João, Porto, Portugal
  • M Teresa Cardoso
    Department of Internal Medicine, Centro Hospitalar Universitário de S. João, Porto, Portugal

Keywords

Cutaneous angiosarcoma, lower limbs, predisposing factors, immunohistochemistry

Abstract

Cutaneous angiosarcoma is a rare, highly malignant tumour of vascular endothelial origin. It usually arises in the skin and superficial soft tissue, mostly on the head and neck. It presents as a variety of lesions, and so is considered a great mimicker, leading to a delay in diagnosis and evidencing the importance of biopsy with immunohistochemistry confirmation. There are few reports of extremity involvement in patients with pre-existing chronic lymphoedema, or exposure to radiation therapy. We report the case of an 82-year-old woman with lower limb extensive cutaneous involvement, distant metastatic disease, and poor therapy response. Its rare location without predisposing factors highlights the need to raise awareness about this disease

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    Published: 2020-09-25
    Issue: 2020: Vol 7 No 12 (view)


    How to cite:
    1.
    Monteiro AO, Branco Ferreira I, César A, Mota A, Pinheiro J, Manuel Lopes J, Cardoso MT. Cutaneous Angiosarcoma in an Unusual Location and Without Predisposing Factors. EJCRIM 2020;7 doi:10.12890/2020_001939.