A Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure?

  • Firdevs Ulutaş Department of Rheumatology, Pamukkale University Faculty of Medicine, Denizli, Turkey
  • Veli Çobankara Department of Rheumatology, Pamukkale University Faculty of Medicine, Denizli, Turkey
  • Aslı Bozdemir Department of Internal Medicine, Pamukkale University Faculty of Medicine, Denizli, Turkey
  • Uğur Karasu Department of Internal Medicine, Pamukkale University Faculty of Medicine, Denizli, Turkey

Keywords

Aortic dissection, antiphospholipid antibody syndrome

Abstract

Systemic lupus erythematosus is a chronic autoimmune disease with a wide variety of clinical presentations induced by different immunocomplexes and autoantibodies. Antiphospholipid antibody syndrome (APLAS) is a life-threatening clinical condition characterized by venous and arterial thromboses or pregnancy morbidity in the presence of persistent moderate/high levels of antiphospholipid antibodies. Aortic dissection is rarely associated with APLAS and always requires prompt diagnosis and early treatment. We report a rare case with a striking presentation. The patient developed multi-organ failure due to lethal aortic dissection and the obstruction of abdominal and thoracic branch vessels.

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Published: 2020-08-27

Issue: Vol 7 No 11 (view)

Section: Articles

How to cite:
1.
Ulutaş F, Çobankara V, Bozdemir A, Karasu U. A Rare Association of Antiphospholipid Antibody Syndrome, Systemic Lupus Erythematosus and Aortic Dissection: A Striking Presentation with Multi-Organ Failure?. EJCRIM 2020;7 doi:10.12890/2020_001887.