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Interrupted Aortic Arch in an Adult
Juliana Silva, Neusa Guiomar, Marisa Passos Silva, Daniel Caeiro, Vasco Gama
http://dx.doi.org/10.12890/2017_000692
European Journal of Case Reports in Internal Medicine - © EFIM

ABSTRACT

Interrupted aortic arch (IAA) is a rare congenital abnormality with only a few cases reported in adults. It is defined as complete loss of continuity between the ascending and descending portions of the aorta, and is usually associated with other cardiac defects. The diagnosis in adults should be suspected in the presence of refractory hypertension, a careful physical examination being crucial to early diagnosis. Magnetic resonance angiography (MRA) techniques can accurately characterize cardiovascular anatomy, and also provide information regarding heart chamber and valve function.

KEYWORDS

Interrupted aortic arch, refractory hypertension, bicuspid aortic valve, aortic coarctation

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