DOI: 10.12890/2024_004505

Sudden cardiac arrest as first manifestation of malignant mitral valve prolapse in a young patient: a case report and review of the literature

Authors

  • Leila Bigdelu Cardiovascular Medicine Division, Vascular Surgery Research Center, Mashhad University of Medical Sciences, Mashhad, Iran
  • Zouheir Bitar Critical Care Unit, Internal Medical Department, Ahmadi Hospital-Kuwait Oil Company, Kuwait
  • Ossama Maadarani Critical Care Unit, Internal Medical Department, Ahmadi Hospital-Kuwait Oil Company, Kuwait

omaadarani@kockw.com

Keywords

Mitral valve prolapse, malignant phenotype, sudden cardiac death

Abstract

Mitral valve prolapse (MVP) is a primary valvular disease of the mitral valve with a prevalence of 2.4% of the general population. Valve abnormalities range from simple fibroelastic deficiency of the leaflets to diffuse myxomatous degenerative changes. MVP is a usually a benign condition. However, the scattered reports of sudden cardiac death in patients with MVP in the absence of severe mitral insufficiency or coronary artery disease suggest the existence of a malignant phenotype of MVP. We report a case of a young female who survived life-threatening arrhythmias and cardiac arrest and was found to have characteristic features of the malignant phenotype of MVP and had an implantable cardioverter defibrillator as a secondary prevention.

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References

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Published

2024-04-03

Issue

Vol. 11 No. 5 (2024)

Categories

How to Cite

1.
Bigdelu L, Bitar Z, Maadarani O. Sudden cardiac arrest as first manifestation of malignant mitral valve prolapse in a young patient: a case report and review of the literature. EJCRIM [Internet]. 2024 Apr. 3 [cited 2026 Nov. 4];11(5). Available from: https://ejcrim.com/index.php/ejcrim/article/view/4505

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