Congenital Inferior Vena Cava Agenesis with Ulceration and Deep Vein Thrombosis
  • Melanie Menning
    Department of Family Medicine, University of Nebraska Medical Center, Omaha, Nebraska, USA
  • Mira Yousef
    College of Medicine, University of Nebraska Medical Center, Omaha, Nebraska, USA

Keywords

Inferior vena cava atresia, IVCA, ulcers, deep vein thrombus, DVT

Abstract

Objectives: This is one of the few case reports of congenital inferior vena cava atresia (IVCA) with extensive bilateral lower extremity ulcers.

Background: IVCA is a congenital anomaly characterized by poor venous return in the lower extremities with increased risk of deep vein thrombi (DVTs) and, rarely, non-healing ulcers.

Results: A 45-year-old woman with history significant for DVTs presented with extensive bilateral lower extremity ulcers, and a CT scan revealed congenital IVCA. Oedema management, DVT prevention, routine wound care and skin grafts resolved the ulcers.

Conclusion: Congenital venous abnormalities should be included in the differential diagnosis of multiple unprovoked DVTs and non-healing ulcers.

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    Published: 2021-03-18
    Issue: 2021: Vol 8 No 3 (view)

    How to cite:
    1.
    Menning M, Yousef M. Congenital Inferior Vena Cava Agenesis with Ulceration and Deep Vein Thrombosis. EJCRIM 2021;8 doi:10.12890/2021_002312.