Hemophagocytic Lymphohistiocytosis Complicating Myelodysplasia

  • Geraldine Quintero-Platt Internal Medicine Department, Canary Islands University Hospital, La Laguna University, Tenerife, Canary Islands
  • Carima Belleyo-Belkasem Internal Medicine Department, Canary Islands University Hospital, La Laguna University, Tenerife, Canary Islands
  • Taida Martín-Santos Hematology Department, Canary Islands University Hospital, La Laguna University, Tenerife, Canary Islands
  • Onán Pérez-Hernández Internal Medicine Department, Canary Islands University Hospital, La Laguna University, Tenerife, Canary Islands
  • Emilio González-Reimers Internal Medicine Department, Canary Islands University Hospital, La Laguna University, Tenerife, Canary Islands

Abstract

We describe a 62-year-old patient with a 4-year history of myelodysplasia who later developedstriking features that included massive splenomegaly, rapidly evolving visual loss and a sensorimotor polyneuropathy. This led us to consider the diagnosisof haemophagocytic lymphohistiocytosis (HLH). Upon further investigation, we found that he fulfilled the necessarydiagnostic criteria for HLH, including the presence of haemophagocytosis of erythroid precursors on bone marrow smear.

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Published: 2014-03-28

Issue: Vol. 1 (2014) (view)

Section: Articles

How to cite:
1.
Quintero-Platt G, Belleyo-Belkasem C, Martín-Santos T, Pérez-Hernández O, González-Reimers E. Hemophagocytic Lymphohistiocytosis Complicating Myelodysplasia. EJCRIM [Internet]. 2014Mar.28 [cited 2020Sep.26];1(1). Available from: https://ejcrim.com/index.php/EJCRIM/article/view/16