Type B Interrupted Aortic Arch with a Patent Ductus Arteriosus in an Adult Presenting with Secondary Polycythaemia

  • Jonan Chun Yin Lee Department of Radiology & Imaging, Queen Elizabeth Hospital, Hong Kong, Hong Kong
  • Jeanie Betsy Chiang Department of Radiology & Imaging, Queen Elizabeth Hospital, Hong Kong, Hong Kong
  • Boris Chun Kei Chow Department of Radiology & Imaging, Queen Elizabeth Hospital, Hong Kong, Hong Kong

Keywords

Interrupted aortic arch, congenital heart disease, secondary polycythaemia, computed tomography, magnetic resonance imaging

Abstract

Interrupted aortic arch (IAA) is an extremely rare congenital cyanotic heart disease characterized by complete disruption between the ascending and descending aorta. A patent ductus arteriosus (PDA) or other collateral pathways provide blood flow to the distal descending aorta. Mortality is extremely high at early infancy, particularly after the closure of ductus arteriosus. Survival and presentation in adulthood are extremely rare. Here we illustrate a rare case of type B interrupted aortic arch in an adult who presented with secondary polycythaemia. The blood supply to descending aorta and beyond is almost solely by a patent ductus arteriosus. The case demonstrates the value of multimodality imaging including CT and MRI for diagnosis and treatment planning in these patients.

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  • Published: 2020-02-26

    Issue: Vol 7 No 4 (view)

    Section: Articles

    How to cite:
    1.
    Lee JCY, Chiang JB, Chow BCK. Type B Interrupted Aortic Arch with a Patent Ductus Arteriosus in an Adult Presenting with Secondary Polycythaemia. EJCRIM 2020;7 doi:10.12890/2020_001511.