Interrupted Aortic Arch in an Adult
  • Juliana Silva
    Serviço de Medicina Interna, Centro Hospitalar Vila Nova de Gaia/Espinho
  • Neusa Guiomar
    Serviço de Cardiologia, Centro Hospitalar Vila Nova de Gaia/Espinho, Vila Nova de Gaia
  • Marisa Passos Silva
    Serviço de Cardiologia, Centro Hospitalar Vila Nova de Gaia/Espinho, Vila Nova de Gaia
  • Daniel Caeiro
    Serviço de Cardiologia, Centro Hospitalar Vila Nova de Gaia/Espinho, Vila Nova de Gaia
  • Vasco Gama
    Serviço de Cardiologia, Centro Hospitalar Vila Nova de Gaia/Espinho, Vila Nova de Gaia

Abstract

Interrupted aortic arch (IAA) is a rare congenital abnormality with only a few cases reported in adults. It is defined as complete loss of continuity between the ascending and descending portions of the aorta, and is usually associated with other cardiac defects. The diagnosis in adults should be suspected in the presence of refractory hypertension, a careful physical examination being crucial to early diagnosis. Magnetic resonance angiography (MRA) techniques can accurately characterize cardiovascular anatomy, and also provide information regarding heart chamber and valve function.

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    Published: 2017-08-03
    Issue: Vol. 4 No. 9 (view)


    How to cite:
    1.
    Silva J, Guiomar N, Silva MP, Caeiro D, Gama V. Interrupted Aortic Arch in an Adult. EJCRIM 2017;4 doi:10.12890/2017_000692.