Eosinophilic Fasciitis: an Atypical Presentation of a Rare Disease
  • Sabrina Poradosu
    Department of Internal Medicine Vrij Universitair Ziekenhuis Brussel (Free University Hospital Brussels) Laarbeeklaan 101, 1090 Brussels
  • Esther Vanderlinden
    Department of Pathology Algemeen Stedelijk Ziekenhuis Aalst Merestraat 80, 9300 Aalst
  • Alex Michotte
    Department of Neurology and Pathology (Neuropathology), Universitair Ziekenhuis Brussel Laarbeeklaan 101, 1090 Brussels
  • Hendrik De Raeve
    Department of Pathology Universitair Ziekenhuis Brussel Laarbeeklaan 101, 1090 Brussels
  • Sabine D Allard
    Department of Internal Medicine, Universitair Ziekenhuis Brussel, Belgium Laarbeeklaan 101, 1090 Brussels

Abstract

Objectives: We report an atypical presentation of eosinophilic fasciitis and provide a concise overview of the literature.

Materials and Methods: Clinical and laboratory findings in a patient presenting with fever and skin induration were recorded. A deep muscle biopsy was performed in order to confirm the diagnosis.

Results: A spontaneous favourable clinical and radiological evolution was observed.

Conclusion: The diagnosis of eosinophilic fasciitis is challenging due to the lack of pathognomonic signs and symptoms. As spontaneous resolution has been described, watchful waiting is defendable depending on the clinical presentation. Although magnetic resonance imaging (MRI) can be useful in establishing the diagnosis, a deep muscle biopsy remains the gold standard diagnostic tool.

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    Published: 2015-04-03
    Issue: Vol. 2 No. 2 (2015) (view)

    How to cite:
    1.
    Poradosu S, Vanderlinden E, Michotte A, De Raeve H, Allard SD. Eosinophilic Fasciitis: an Atypical Presentation of a Rare Disease. EJCRIM 2015;2 doi:10.12890/2015_000186.

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